Alpha-1 antitrypsin deficiency panniculitis

Alpha-1 antitrypsin deficiency panniculitis (also known as "Alpha1-protease deficiency panniculitis," and "Alpha1-proteinase deficiency panniculitis"^[1]) is a skin condition characterized by inflammation of the subcutaneous fat associated with a deficiency of the α₁-antitrypsin enzyme.^[2]^:494

References

^ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0.
^ James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0.

Disorders of subcutaneous fat (M79.3, 729.3)

Panniculitis

Lobular	without vasculitis: Cytophagic histiocytic panniculitis · Factitial panniculitis · Gouty panniculitis · Pancreatic panniculitis · Traumatic panniculitis (Cold panniculitis) · needle-shaped clefts (Subcutaneous fat necrosis of the newborn, Sclerema neonatorum, Post-steroid panniculitis) · Lipodermatosclerosis · Weber–Christian disease · Lupus erythematosus panniculitis · Sclerosing lipogranuloma with vasculitis: Nodular vasculitis/Erythema induratum

Septal	without vasculitis: Alpha-1 antitrypsin deficiency panniculitis · Erythema nodosum (Acute erythema nodosum, Chronic erythema nodosum) with vasculitis: Superficial thrombophlebitis

Lipodystrophy

Acquired	generalized: Acquired generalized lipodystrophy partial: Acquired partial lipodystrophy · Centrifugal abdominal lipodystrophy · HIV-associated lipodystrophy · Lipoatrophia annularis localized: Localized lipodystrophy

Congenital	Congenital generalized lipodystrophy · Familial partial lipodystrophy Poland's syndrome

M: INT, SF, LCT

anat/phys/devp

noco(i/b/d/q/u/r/p/m/k/v/f)/cong/tumr(n/e/d), sysi/epon

proc, drug (D2/3/4/5/8/11)

Alpha-1 antitrypsin deficiency panniculitis

See also

References